Sirenomelia: A Rare Malformation
نویسندگان
چکیده
A twenty two year old primigravida, at thirty four weeks gestation delivered a 1.7 kg baby by emergency lower segment cesarean section. Cesarean section was done in view of severe intrauterine growth retardation and severe oligohydramnios. There was no history of diabetes mellitus or gestational diabetes in the mother, no history of any chronic medical illness, any drug intake or consanguinity in mother and no history of any genetic disorder in family. Only one prenatal ultrasound was done in first trimester which was reported to be normal. Baby did not cry at birth and required resuscitation. APGAR score was 5, 7 and 7 at 1, 5 and 10 minutes respectively. Baby had two umbilical arteries.
منابع مشابه
Sirenomelia – a Case Report
Mermaid baby also known as sirenomelia is a rare and usually lethal congenital abnormality with multisystem involvement. Characteristic feature consists of varying degrees of lower limb fusion which in severe form results in single lower limb with nondiscernible limb bones. We herein report a case of sirenomelia with variable malformation. Key-Words: Sirenomelia, Mermaid Syndrome
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